Product Description
DES (Desmin ) monoclonal Antibody | MB63007 | Bioworld
Host: Mouse
Reactivity: Human, Mouse, Rat
Application: FC, IHC, WB
Application Range: WB 1:200~500, IHC 1:150, FLOW 1:100
Background: This gene encodes a muscle-specific class III intermediate filament. Homopolymers of this protein form a stable intracytoplasmic filamentous network connecting myofibrils to each other and to the plasma membrane. Mutations in this gene are associated with desmin-related myopathy, a familial cardiac and skeletal myopathy (CSM), and with distal myopathies. [provided by RefSeq, Jul 2008]
Storage & Stability: PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.
Specificity: desmin
Molecular Weight: 53.4 kDa (Predicted)
Note: For research use only, not for use in diagnostic procedure.
Alternative Names: CSM1; CSM2; LGMD2R
Immunogen: Human fragment corresponding to amino acids 104-391 of human DES (NP_001918) produced in E.coli.
Conjugate: Unconjugated
Modification: Unmodification
Purification & Purity: Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G)
Pathway: N/A